Plexiform Neurofibroma

2
Pipeline Programs
2
Companies
2
Clinical Trials
0
Approved Products

Pipeline by Development Stage

Preclinical
Phase 1
Phase 1/2
Phase 2
Phase 2/3
Phase 3
On Market
0
0
0
1
0
1
0
Early DiscoveryClinical DevelopmentMarket

Drug Modality Breakdown

Small Molecule
1100%
+ 1 programs with unclassified modality

Competitive Landscape

2 companies ranked by most advanced pipeline stage

CT
1 program
1
TQ-B3234 capsulesPhase 31 trial
Active Trials
NCT07407803Not Yet RecruitingEst. Dec 2028
SpringWorks Therapeutics
1 program
1
MirdametinibPhase 2Small Molecule1 trial
Active Trials
NCT03962543Active Not Recruiting114Est. Dec 2028

Trial Timeline

Clinical trial activity over time

2021
2022
2023
2024
2025
2026
2027
2028
Chia Tai TianQing Pharmaceutical GroupTQ-B3234 capsules
SpringWorks TherapeuticsMirdametinib

Clinical Trials (2)

Total enrollment: 114 patients across 2 trials

Evaluation of TQ-B3234 Capsules in Patients With Symptomatic, Non-Surgical Type 1 Neurofibromatosis-Associated Plexiform Neurofibromas

Start: Feb 2026Est. completion: Dec 2028
Phase 3Not Yet Recruiting

MEK Inhibitor Mirdametinib (PD-0325901) in Patients With Neurofibromatosis Type 1 Associated Plexiform Neurofibromas

Start: Sep 2019Est. completion: Dec 2028114 patients
Phase 2Active Not Recruiting

Phase Legend

PreclinicalLab & animal studies
Phase 1Safety & dosing
Phase 2Efficacy testing
Phase 3Large-scale trials
On MarketApproved & available

Key Insights

1 late-stage (Phase 3) programs — potential near-term approvals
Small Molecule is the dominant modality (100% of programs)
2 companies competing in this space