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Lysosomal Storage Disease

0
Pipeline Programs
3
Companies
4
Clinical Trials
0
Approved Products

Pipeline by Development Stage

Preclinical
Phase 1
Phase 1/2
Phase 2
Phase 2/3
Phase 3
On Market
0
0
0
0
0
0
0
Early DiscoveryClinical DevelopmentMarket

Drug Modality Breakdown

Gene Therapy
1100%
+ 3 programs with unclassified modality

Competitive Landscape

3 companies ranked by most advanced pipeline stage

Orchard Therapeutics
2 programs
OTL-200 Gene TherapyPHASE_1_2Gene Therapy1 trial
OTL-200PHASE_21 trial
Active Trials
NCT01560182Completed20Est. Sep 2025
NCT03392987Completed10Est. Mar 2026
CENTOGENE
CENTOGENEGermany - Rostock
1 program
Biomarker for Maroteaux-Lamy Disease (BioMaroteaux)N/A1 trial
Active Trials
NCT01458613Withdrawn0Est. Feb 2021
Human BioSciences
Human BioSciencesWV - Martinsburg
1 program
Study of Inborn Errors of Cholesterol Synthesis and Related DisordersN/A1 trial
Active Trials
NCT00046202Completed342

Trial Timeline

Clinical trial activity over time

2021
2022
2023
2024
2025
2026
Orchard TherapeuticsOTL-200
Orchard TherapeuticsOTL-200 Gene Therapy
CENTOGENEBiomarker for Maroteaux-Lamy Disease (BioMaroteaux)
Human BioSciencesStudy of Inborn Errors of Cholesterol Synthesis and Related Disorders

Clinical Trials (4)

Total enrollment: 372 patients across 4 trials

A Safety and Efficacy Study of Cryopreserved OTL-200 for Treatment of Metachromatic Leukodystrophy (MLD)

Start: Jan 2018Est. completion: Mar 202610 patients
Phase 2Completed

Gene Therapy for Metachromatic Leukodystrophy (MLD)

Start: Apr 2010Est. completion: Sep 202520 patients
Phase 1/2Completed
NCT01458613CENTOGENEBiomarker for Maroteaux-Lamy Disease (BioMaroteaux)

Biomarker for Maroteaux-Lamy Disease (BioMaroteaux)

Start: Aug 2018Est. completion: Feb 20210
N/AWithdrawn
NCT00046202Human BioSciencesStudy of Inborn Errors of Cholesterol Synthesis and Related Disorders

Study of Inborn Errors of Cholesterol Synthesis and Related Disorders

Start: Oct 2002342 patients
N/ACompleted

Phase Legend

PreclinicalLab & animal studies
Phase 1Safety & dosing
Phase 2Efficacy testing
Phase 3Large-scale trials
On MarketApproved & available

Key Insights

3 companies competing in this space

The information on this page is for informational purposes only and should not be used as a substitute for professional medical advice. Drug information is sourced from FDA, DailyMed, and other government databases. Adverse event data from FAERS does not establish causation. Always consult a healthcare professional for medical decisions.